A 9-year-old girl with unsteady gait and weakness in lower limbs is likely suffering from which condition?

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The presentation of unsteady gait and weakness in the lower limbs in a 9-year-old girl is most consistent with Friedreich ataxia. This is a hereditary degenerative disease that typically manifests in childhood or early adulthood and is characterized by progressive ataxia, which is a loss of coordination, as well as weakness in the legs due to involvement of the spinal cord and peripheral nerves. The unsteady gait is a direct result of the ataxia, while the weakness can be attributed to muscular and neurological degeneration associated with the condition.

Patients with Friedreich ataxia often also exhibit other neurological signs such as scoliosis, loss of deep tendon reflexes, and sensory abnormalities. Since this condition is hereditary, a history of similar symptoms in relatives can often be noted.

In contrast, multiple sclerosis is less common in this age group and typically presents later in life, often with more varied neurological symptoms. Cerebral palsy results from perinatal brain injuries and would usually present with spasticity rather than ataxia and would typically not progress in the way Friedreich ataxia does. Muscular dystrophy, while causing weakness, usually presents with proximal weakness rather than the characteristic gait disturbance seen in ataxia. Therefore, given the

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