How does osteogenesis imperfecta primarily affect dentition?

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Osteogenesis imperfecta (OI), a genetic disorder characterized by fragile bones, also significantly impacts dentition due to its effect on collagen, which is an essential component of tooth structure. In individuals with OI, teeth often appear opalescent, meaning they have a translucent quality with a blue or gray tint. This unique appearance is attributed to defects in the collagen matrix that affect the dental enamel and dentin, leading to the characteristic color and translucence.

Additionally, these dental changes can increase susceptibility to dental issues such as caries and fractures. While discolored teeth can occur due to various reasons, in the context of OI, the hallmark feature is the opalescent appearance rather than simple discoloration. Overly dense teeth or absent teeth are not typical presentations associated with osteogenesis imperfecta, as the condition does not lead to an increase in tooth density and tooth absence is not a defining characteristic of the disorder's impact on dental health.

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